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ILAE classification of the epilepsies: Position paper of the ILAE Commission for Classification and Terminology.

Identifieur interne : 000A52 ( Main/Exploration ); précédent : 000A51; suivant : 000A53

ILAE classification of the epilepsies: Position paper of the ILAE Commission for Classification and Terminology.

Auteurs : Ingrid E. Scheffer [Australie] ; Samuel Berkovic [Australie] ; Giuseppe Capovilla [Italie] ; Mary B. Connolly [Canada] ; Jacqueline French [États-Unis] ; Laura Guilhoto [Brésil] ; Edouard Hirsch [France] ; Satish Jain [Inde] ; Gary W. Mathern [États-Unis] ; Solomon L. Moshé [États-Unis] ; Douglas R. Nordli [États-Unis] ; Emilio Perucca [Italie] ; Torbjörn Tomson [Suède] ; Samuel Wiebe [Canada] ; Yue-Hua Zhang [République populaire de Chine] ; Sameer M. Zuberi [Royaume-Uni]

Source :

RBID : pubmed:28276062

Descripteurs français

English descriptors

Abstract

The International League Against Epilepsy (ILAE) Classification of the Epilepsies has been updated to reflect our gain in understanding of the epilepsies and their underlying mechanisms following the major scientific advances that have taken place since the last ratified classification in 1989. As a critical tool for the practicing clinician, epilepsy classification must be relevant and dynamic to changes in thinking, yet robust and translatable to all areas of the globe. Its primary purpose is for diagnosis of patients, but it is also critical for epilepsy research, development of antiepileptic therapies, and communication around the world. The new classification originates from a draft document submitted for public comments in 2013, which was revised to incorporate extensive feedback from the international epilepsy community over several rounds of consultation. It presents three levels, starting with seizure type, where it assumes that the patient is having epileptic seizures as defined by the new 2017 ILAE Seizure Classification. After diagnosis of the seizure type, the next step is diagnosis of epilepsy type, including focal epilepsy, generalized epilepsy, combined generalized, and focal epilepsy, and also an unknown epilepsy group. The third level is that of epilepsy syndrome, where a specific syndromic diagnosis can be made. The new classification incorporates etiology along each stage, emphasizing the need to consider etiology at each step of diagnosis, as it often carries significant treatment implications. Etiology is broken into six subgroups, selected because of their potential therapeutic consequences. New terminology is introduced such as developmental and epileptic encephalopathy. The term benign is replaced by the terms self-limited and pharmacoresponsive, to be used where appropriate. It is hoped that this new framework will assist in improving epilepsy care and research in the 21st century.

DOI: 10.1111/epi.13709
PubMed: 28276062


Affiliations:


Links toward previous steps (curation, corpus...)


Le document en format XML

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</keywords>
<keywords scheme="MESH" qualifier="classification" xml:lang="en">
<term>Epilepsy</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en">
<term>Epilepsy</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr">
<term>Épilepsie</term>
</keywords>
<keywords scheme="MESH" qualifier="etiology" xml:lang="en">
<term>Epilepsy</term>
</keywords>
<keywords scheme="MESH" qualifier="étiologie" xml:lang="fr">
<term>Épilepsie</term>
</keywords>
<keywords scheme="MESH" xml:lang="en">
<term>Humans</term>
<term>International Agencies</term>
<term>Terminology as Topic</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr">
<term>Agences internationales</term>
<term>Humains</term>
<term>Terminologie comme sujet</term>
<term>Épilepsie</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">The International League Against Epilepsy (ILAE) Classification of the Epilepsies has been updated to reflect our gain in understanding of the epilepsies and their underlying mechanisms following the major scientific advances that have taken place since the last ratified classification in 1989. As a critical tool for the practicing clinician, epilepsy classification must be relevant and dynamic to changes in thinking, yet robust and translatable to all areas of the globe. Its primary purpose is for diagnosis of patients, but it is also critical for epilepsy research, development of antiepileptic therapies, and communication around the world. The new classification originates from a draft document submitted for public comments in 2013, which was revised to incorporate extensive feedback from the international epilepsy community over several rounds of consultation. It presents three levels, starting with seizure type, where it assumes that the patient is having epileptic seizures as defined by the new 2017 ILAE Seizure Classification. After diagnosis of the seizure type, the next step is diagnosis of epilepsy type, including focal epilepsy, generalized epilepsy, combined generalized, and focal epilepsy, and also an unknown epilepsy group. The third level is that of epilepsy syndrome, where a specific syndromic diagnosis can be made. The new classification incorporates etiology along each stage, emphasizing the need to consider etiology at each step of diagnosis, as it often carries significant treatment implications. Etiology is broken into six subgroups, selected because of their potential therapeutic consequences. New terminology is introduced such as developmental and epileptic encephalopathy. The term benign is replaced by the terms self-limited and pharmacoresponsive, to be used where appropriate. It is hoped that this new framework will assist in improving epilepsy care and research in the 21st century.</div>
</front>
</TEI>
<affiliations>
<list>
<country>
<li>Australie</li>
<li>Brésil</li>
<li>Canada</li>
<li>France</li>
<li>Inde</li>
<li>Italie</li>
<li>Royaume-Uni</li>
<li>République populaire de Chine</li>
<li>Suède</li>
<li>États-Unis</li>
</country>
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<li>Alberta</li>
<li>Alsace (région administrative)</li>
<li>Californie</li>
<li>Grand Est</li>
<li>Svealand</li>
<li>Victoria (État)</li>
<li>État de New York</li>
<li>État de São Paulo</li>
</region>
<settlement>
<li>Calgary</li>
<li>Melbourne</li>
<li>Pékin</li>
<li>Stockholm</li>
<li>Strasbourg</li>
<li>São Paulo</li>
</settlement>
<orgName>
<li>Université de Calgary</li>
<li>Université de Melbourne</li>
</orgName>
</list>
<tree>
<country name="Australie">
<region name="Victoria (État)">
<name sortKey="Scheffer, Ingrid E" sort="Scheffer, Ingrid E" uniqKey="Scheffer I" first="Ingrid E" last="Scheffer">Ingrid E. Scheffer</name>
</region>
<name sortKey="Berkovic, Samuel" sort="Berkovic, Samuel" uniqKey="Berkovic S" first="Samuel" last="Berkovic">Samuel Berkovic</name>
</country>
<country name="Italie">
<noRegion>
<name sortKey="Capovilla, Giuseppe" sort="Capovilla, Giuseppe" uniqKey="Capovilla G" first="Giuseppe" last="Capovilla">Giuseppe Capovilla</name>
</noRegion>
<name sortKey="Perucca, Emilio" sort="Perucca, Emilio" uniqKey="Perucca E" first="Emilio" last="Perucca">Emilio Perucca</name>
</country>
<country name="Canada">
<noRegion>
<name sortKey="Connolly, Mary B" sort="Connolly, Mary B" uniqKey="Connolly M" first="Mary B" last="Connolly">Mary B. Connolly</name>
</noRegion>
<name sortKey="Wiebe, Samuel" sort="Wiebe, Samuel" uniqKey="Wiebe S" first="Samuel" last="Wiebe">Samuel Wiebe</name>
</country>
<country name="États-Unis">
<region name="État de New York">
<name sortKey="French, Jacqueline" sort="French, Jacqueline" uniqKey="French J" first="Jacqueline" last="French">Jacqueline French</name>
</region>
<name sortKey="Mathern, Gary W" sort="Mathern, Gary W" uniqKey="Mathern G" first="Gary W" last="Mathern">Gary W. Mathern</name>
<name sortKey="Moshe, Solomon L" sort="Moshe, Solomon L" uniqKey="Moshe S" first="Solomon L" last="Moshé">Solomon L. Moshé</name>
<name sortKey="Nordli, Douglas R" sort="Nordli, Douglas R" uniqKey="Nordli D" first="Douglas R" last="Nordli">Douglas R. Nordli</name>
</country>
<country name="Brésil">
<region name="État de São Paulo">
<name sortKey="Guilhoto, Laura" sort="Guilhoto, Laura" uniqKey="Guilhoto L" first="Laura" last="Guilhoto">Laura Guilhoto</name>
</region>
</country>
<country name="France">
<region name="Grand Est">
<name sortKey="Hirsch, Edouard" sort="Hirsch, Edouard" uniqKey="Hirsch E" first="Edouard" last="Hirsch">Edouard Hirsch</name>
</region>
</country>
<country name="Inde">
<noRegion>
<name sortKey="Jain, Satish" sort="Jain, Satish" uniqKey="Jain S" first="Satish" last="Jain">Satish Jain</name>
</noRegion>
</country>
<country name="Suède">
<region name="Svealand">
<name sortKey="Tomson, Torbjorn" sort="Tomson, Torbjorn" uniqKey="Tomson T" first="Torbjörn" last="Tomson">Torbjörn Tomson</name>
</region>
</country>
<country name="République populaire de Chine">
<noRegion>
<name sortKey="Zhang, Yue Hua" sort="Zhang, Yue Hua" uniqKey="Zhang Y" first="Yue-Hua" last="Zhang">Yue-Hua Zhang</name>
</noRegion>
</country>
<country name="Royaume-Uni">
<noRegion>
<name sortKey="Zuberi, Sameer M" sort="Zuberi, Sameer M" uniqKey="Zuberi S" first="Sameer M" last="Zuberi">Sameer M. Zuberi</name>
</noRegion>
</country>
</tree>
</affiliations>
</record>

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